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НЕКОМПАКТНЫЙ МИОКАРД ЛЕВОГО ЖЕЛУДОЧКА: СИМПТОМ, СИНДРОМ ИЛИ ВАРИАНТ РАЗВИТИЯ?

https://doi.org/10.15829/1560-4071-2017-2-106-113

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Аннотация

Синдром некомпактного миокарда левого желудочка — относительно новый диагноз, вошедший в клиническую практику с усовершенствованием методов визуализации сердца. Проводится большое количество исследований, посвященных генетическому разнообразию синдрома некомпактного миокарда и его вкладу в течение различных ассоциированных кардиомиопатий. Однако единого мнения о патогенезе некомпактности миокарда нет, как нет и единых диагностических критериев, и руководства по лечению и динамическому наблюдению пациентов с СНМЛЖ. В настоящем обзоре мы обобщаем данные о природе этого состояния, его генетических причинах, о диагностике и лечении.

Об авторах

М. Е. Поляк
ФГБНУ Российский научный центр хирургии им. акад. Б.В. Петровского, Москва
Россия
врач-генетик, лаборатория медицинской генетики


Е. А. Мершина
ФГАУ Лечебно-реабилитационный центр Минздрава России, Москва
Россия
к.м.н., зав. отделом томографии Центра лучевой диагностики


Е. В. Заклязьминская
ФГБНУ Российский научный центр хирургии им. акад. Б.В. Петровского, Москва; ФГБОУ Российский национальный исследовательский медицинский университет им. Н.И. Пирогова, Москва
Россия

лаборатория медицинской генетики

д.м.н., зав. лабораторией,

медико-биологический факультет

кафедра молекулярной и клеточной генетики 

доцент 



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Для цитирования:


Поляк М.Е., Мершина Е.А., Заклязьминская Е.В. НЕКОМПАКТНЫЙ МИОКАРД ЛЕВОГО ЖЕЛУДОЧКА: СИМПТОМ, СИНДРОМ ИЛИ ВАРИАНТ РАЗВИТИЯ? Российский кардиологический журнал. 2017;(2):106-113. https://doi.org/10.15829/1560-4071-2017-2-106-113

For citation:


Polyak M.E., Mershina E.A., Zaklyazminskaya E.V. NON-COMPACTION LEFT VENTRICLE MYOCARDIUM: A SYMPTOM, SYNDROME OR DEVELOPMENT VARIATION? Russian Journal of Cardiology. 2017;(2):106-113. (In Russ.) https://doi.org/10.15829/1560-4071-2017-2-106-113

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ISSN 1560-4071 (Print)
ISSN 2618-7620 (Online)