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CASE OF PRIMARY AMYLOIDOSIS WITH INVOLVEMENT OF THE HEART AND PERICARDIUM IN CARDIOLOGY PRACTICE

https://doi.org/10.15829/1560-4071-2017-2-103-105

Abstract

In the article, a case presented of primary amyloidosis of the heart and pericardium, with severe resistant heart failure. That kind of case witnesses that diagnostics and management of patients with this disease, is a complicated issue in cardiology practice. That is related to its rarity, absence of key simptoms in clinical practice and delayed diagnostics with lack of expected efficacy of modern treatment.

About the Authors

I. V. Demko
V. F. Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk
Russian Federation


L. I. Pelinovskaya
V. F. Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk
Russian Federation


V. A. Mosina
V. F. Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk
Russian Federation


A. Y. Kraposhina
V. F. Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk
Russian Federation


N. V. Gordeeva
V. F. Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk
Russian Federation


I. A. Solovyova
V. F. Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk
Russian Federation


A. E. Ryazanov
Regional Clinical Hospital, Krasnoyarsk
Russian Federation


References

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2. Zhdanova EA, Gudkova KV, Rameev VV i dr. Sovremennye predstavlenija ob amiloidoze serdca. Kardiologija 2013; 12: 70-78. Russian (Жданова ЕА, Гудкова КВ, Рамеев ВВ и др. Современные представления об амилоидозе сердца. Кардиология 2013; 12: 70-78.)

3. Volkova EN, Posnenkova OM, Popova YuV i dr. Clinical case of the advanced form of primary amyloidosis with a heart lesion. Byulleten' meditsinskikh internet-konferentsiy 2014; 4(9): 1038-1041. Russian (Волкова ЕН, Посненкова ОМ, Попова ЮВ и др. Клинический случай запущенной формы первичного амилоидоза с поражением сердца. Бюллетень медицинских интернет-конференций 2014; 4(9): 1038-1041.)

4. Novikova ON, Rudenko EA, Alekseeva NV i dr. Difficulties of diagnostics of an amyloid cardiopathy. A case from practice. Klinicheskaya praktika 2014; 1(17): 38-43. Russian (Новикова ОН, Руденко ЕА, Алексеева НВ и др. Сложности диагностики амилоидной кардиопатии. Случай из практики. Клиническая практика 2014; 1(17): 38-43.)

5. Uholkina GB, Kuchin GA, Bychkova OP i dr. Amyloidosis of the heart in clinical practice. Zhurnal serdechnaja nedostatochnost' 2016; 1: 57-68. Russian (Ухолкина ГБ, Кучин ГА, Бычкова ОП и др. Амилоидоз сердца в клинической практике. Журнал сердечная недостаточность 2016; 1: 57-68.)

6. Gillmore JD, Wechale A, Bird J et al. Guidelines on the diagnosis and investigation of AL amyloidosis. Br J Haematol 2015; 168(2): 207-218.

7. Tereshchenko YuA, Panchenko TL, Matveeva IV. Primary amyloidosis: the difficulties of diagnosis. Sibirskoe meditsinskoe obozrenie 2010; 5(65): 73-76. Russian (Терещенко ЮА, Панченко ТЛ, Матвеева ИВ. Первичный амилоидоз: трудности диагноза. Сибирское медицинское обозрение 2010; (65): 73-76.)


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For citations:


Demko I.V., Pelinovskaya L.I., Mosina V.A., Kraposhina A.Y., Gordeeva N.V., Solovyova I.A., Ryazanov A.E. CASE OF PRIMARY AMYLOIDOSIS WITH INVOLVEMENT OF THE HEART AND PERICARDIUM IN CARDIOLOGY PRACTICE. Russian Journal of Cardiology. 2017;(2):103-105. (In Russ.) https://doi.org/10.15829/1560-4071-2017-2-103-105

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ISSN 1560-4071 (Print)
ISSN 2618-7620 (Online)