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СОСУДИСТАЯ ПАТОЛОГИЯ ПРИ НАСЛЕДУЕМЫХ НАРУШЕНИЯХ СОЕДИНИТЕЛЬНОЙ ТКАНИ

https://doi.org/10.15829/1560-4071-2013-2-83-88

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Аннотация

Группа наследуемых нарушений соединительной ткани включает несколько сотен генетически гетерогенных заболеваний, характеризующихся системными повреждениями соединительно-тканных структур, клинический набор которых зависит от характера мутации. Среди них есть как давно описанные и широко известные состояния – такие, как синдромы Марфана и Элерса-Данло, так и заболевания, описанные сравнительно недавно и, в силу этого, известные в меньшей степени. В клиническую картину многих из этих синдромов входят сосудистые повреждения, прежде всего аорты и артериального русла, которым и посвящен данный обзор.

Об авторах

М. А. Перекальская
ГБОУ ВПО Новосибирский государственный медицинский университет МЗ и СР РФ
Россия
д. м.н., профессор, зав. кафедрой внутренних болезней


И. И. Волкова
ФГБУ ННИИПК им. акад. Е. Н. Мешалкина МЗ и СР РФ
Россия
к. м.н., зав. научно-организационным отделом


Ю. О. Останина
ГБОУ ВПО Новосибирский государственный медицинский университет МЗ и СР РФ
Россия

аспирант кафедры госпитальной терапии и клинической фармакологии



Е. Б. Лукша
ГБУЗ НСО ГНОКДЦ, Новосибирск, Россия
Россия

к. м.н., зав. отделением кардиологических и сосудистых методов исследования



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Для цитирования:


Перекальская М.А., Волкова И.И., Останина Ю.О., Лукша Е.Б. СОСУДИСТАЯ ПАТОЛОГИЯ ПРИ НАСЛЕДУЕМЫХ НАРУШЕНИЯХ СОЕДИНИТЕЛЬНОЙ ТКАНИ. Российский кардиологический журнал. 2013;(2):83-88. https://doi.org/10.15829/1560-4071-2013-2-83-88

For citation:


Perekalskaya M.A., Volkova I.I., Ostanina Y.O., Luksha E.B. Vascular pathology in hereditary connective tissue disorders. Russian Journal of Cardiology. 2013;(2):83-88. (In Russ.) https://doi.org/10.15829/1560-4071-2013-2-83-88

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