FIRST EXPERIENCE OF BOSENTAN IN COMPLEX MANAGEMENT OF A CHILD WITH VENA GALENI ANEURYSM
https://doi.org/10.15829/1560-4071-2017-1-114-120
Abstract
During postnatal period, the causes of progressing heart failure are not only the inborn defects or cardiac rhythm disorders, but extracardiac diseases as well. Among such pathologies are the arterial-venous malformations of the brain vessels, including vena Galeni aneurysm. Inside the aneurysmatic sacks of the brain vessels, up to 80% of blood ejected from the left ventricle could be shunted, which leads then through the right chambers and causes heart failure and pulmonary hypertension. Recent drug treatment makes it to effectively treat pulmonary hypertension, compensate the signs of heart failure and stabilize the condition of a newborn before surgery. The case presented, is a bright evidence of this.
About the Authors
I. I. Trunina
Bashlyaeva Z.A. Pediatric City Clinical Hospital;
N. I. Pirogov Russian National Research Medical University (RNRMU)
Russian Federation
Moscow
Russian Federation
Moscow
A. S. Sharykin
Bashlyaeva Z.A. Pediatric City Clinical Hospital;
N. I. Pirogov Russian National Research Medical University (RNRMU)
Russian Federation
Moscow
Russian Federation
Moscow
M. I. Livshits
Morozov Pediatric City Clinical Hospital
Russian Federation
Moscow
Russian Federation
Moscow
T. R. Lavrova
Bashlyaeva Z.A. Pediatric City Clinical Hospital
Russian Federation
Moscow
Russian Federation
Moscow
I. M. Osmanov
Bashlyaeva Z.A. Pediatric City Clinical Hospital
Russian Federation
Moscow
Russian Federation
Moscow
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Review
For citations:
Trunina I.I., Sharykin A.S., Livshits M.I., Lavrova T.R., Osmanov I.M. FIRST EXPERIENCE OF BOSENTAN IN COMPLEX MANAGEMENT OF A CHILD WITH VENA GALENI ANEURYSM. Russian Journal of Cardiology. 2017;(1):114-120. (In Russ.) https://doi.org/10.15829/1560-4071-2017-1-114-120
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