russjcardiolРоссийский кардиологический журналRussian Journal of Cardiology1560-40712618-7620«SILICEA-POLIGRAF» LLC10.15829/1560-4071-2025-6309KECQMQrussjcardiol-6309Research ArticleПРОБЛЕМНАЯ СТАТЬЯ"Диссинхроническая" кардиомиопатия у пациентов с феноменом Вольфа-Паркинсона-Уайта: решенные и нерешенные проблемыDyssynchrony cardiomyopathy in patients with Wolff-Parkinson-White syndrome: solved and unsolved problemshttps://orcid.org/0000-0003-2469-8098КартофелеваЕ. О.KartofelevaE. O.

Елена Олеговна Картофелева — м.н.с., отделение детской кардиологии

Томск

Tomsk

lenakartofeleva@yandex.ruhttps://orcid.org/0000-0002-2056-4060СвинцоваЛ. И.SvintsovaL. I.

Лилия Ивановна Свинцова — д.м.н., в.с., отделение детской кардиологии

Томск

Tomsk

lis@cardio-tomsk.ruhttps://orcid.org/0000-0002-3947-4903ДжаффароваО. Ю.DzhaffarovaO. Yu.

Ольга Юрьевна Джаффарова — к.м.н., с.н.с., отделение детской кардиологии

Томск

Tomsk

oyd@cardio-tomsk.ruhttps://orcid.org/0009-0001-5928-949XЯкимоваЕ. В.YakimovaE. V.

Евгения Валентиновна Якимова — м.н.с., отделение детской кардиологии

Томск

Tomsk

Evgenia@cardio-tomsk.ruНИИ кардиологии, ФГБНУ Томский НМИЦ Российской академии наукРоссияCardiology Research Institute, Tomsk National Medical Research CenterRussian Federation202514102025309SОбзоры литературы, мнения по проблеме63096309Copyright © Картофелева Е.О., Свинцова Л.И., Джаффарова О.Ю., Якимова Е.В., 20252025Картофелева Е.О., Свинцова Л.И., Джаффарова О.Ю., Якимова Е.В.Kartofeleva E.O., Svintsova L.I., Dzhaffarova O.Y., Yakimova E.V.This work is licensed under a Creative Commons Attribution 4.0 License.https://russjcardiol.elpub.ru/jour/article/view/6309

В статье представлен обзор данных, касающихся формирования кардиомиопатии с дилатационным фенотипом у пациентов с феноменом Вольфа-Паркинсона-Уайта. Показано, у детей раннего возраста с феноменом Вольфа-Паркинсона-Уайта, наиболее выраженной преэкзитацией на электрокардиограмме и правой септальной или правой боковой локализацией дополнительных предсердно-желудочковых соединений, может возникнуть гипотрофия и дискинезия межжелудочковой перегородки, с последующим развитием дилатации и дисфункции левого желудочка. Однако данные факторы не являются специфичные и формирование кардиомиопатии возможно у пациентов любого возраста и при других локализациях дополнительных проводящих путей. Кроме того, в действующих классификациях кардиомиопатий у детей нет понятия, которое включает данное состояние, а также нет критериев для постановки этого диагноза.

The article presents a review on dilated cardiomyopathy in patients with the Wolff-Parkinson-White syndrome. It is shown that in young children with the Wolff-Par-kinson-White syndrome, the most pronounced pre-excitation on the electrocardiogram and the right septal or right lateral location of accessory atrioventricular pathways, hypotrophy and dyskinesia of the interventricular septum may occur, with subsequent left ventricular dilation and dysfunction. However, these factors are not specific and cardiomyopathy development is possible in patients of any age and with other locations of additional conduction pathways. In addition, the current classifications of cardiomyopathies in children do not include a concept that includes this condition, and there are no criteria for making this diagnosis.

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The authors declare that there are no conflicts of interest present.